Orkambi Uses

 The drug is a combination of 2 drugs: lumacaftor and ivacaftor. It is used to treat cystic fibrosis in some people (people with 2 abnormal copies of the "CFTR" gene). It may help improve breathing, reduce the risk of lung infections and improve weight.
How to use Orkambi

Please read the "Patient Information Booklet" provided by the pharmacist before starting to take lumacaftor / ivacaftor and every time you supplement. If you have any questions, please consult your doctor or pharmacist.

Follow your doctor's instructions to take this medication by mouth, usually twice a day (12 hours apart). Eat fat-containing meals or snacks before or immediately after taking the medicine. Examples include eggs, avocados, nuts, butter, peanut butter, cheese pizza or whole milk products (such as whole milk, cheese, yogurt).

If you are taking this medicine in granular form, shake the package gently before use. Open the package and carefully pour the contents into a small bowl containing 1 teaspoon (5ml) of soft food or liquid (such as yogurt, applesauce, pudding, milk or juice). Soft food or liquids should be at or below room temperature. After mixing, absorb all the mixture within 1 hour. Make sure to eat fatty foods as directed.

The dosage depends on your age, medical condition, response to treatment, and other medications you may be taking. Be sure to inform your doctor and pharmacist of all products you use (including prescription drugs, over-the-counter drugs, and herbal products).

Use this medication regularly to get the most benefit. To help you remember, take it at the same time every day. If you temporarily stop taking this medicine for more than 1 week, please consult your doctor for specific instructions on restarting this medicine. If you are taking certain other medications, you may be instructed to restart at a lower dose in the first week.